Objectives: The aim of this study was to examine the incidence of congenial heart defects (CHD) and to determine the frequency of CHD. Furthermore, the study aimed to examine the impact of risk factors and positive family history as well as gender, birth year and characteristics at birth with the emergence of CHD. Study outline: A two-year retrospective study Participants and Methods: The study included 162 children with a diagnosis of congenital heart defects born between 1st Januaty 2014 and 31st December 2015. The data was obtained from the medical records. Results and Conclusions: There was equal number of subjects of both sexes and years of birth. CHD diagnosis is most often given immediately after birth, and the length of the gestation, birth weight and Apgar score are usually within the normal range. There were 44.1% patients with major CHD, and 55.1% patients with minor CHD. Significantly more often minor CHD was found and ventricular septal defect is the most common CHD (45.2%). Second most common CHD is persistent ductus arteriosus, which is somewhat more common in male respondents. There is a significant association between genetic syndromes and the appearance of CHD. The most common syndrome is Down syndrome (17.7%), which highlights the ventricular septal defect, tricuspid insufficiency and atrioventricular septal defect. Risk factors set forth the 48.4% of respondents, such as positive family history, the CHD have 6.5%, i.e. 9.7% of the genetic syndromes. Foramen ovale is more frequent minor CHD (97.4%) and significant difference in gender and age distribution was not found.